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Acta Neurochirurgica
Published in: Acta Neurochirurgica 2/2021

01-02-2021 | Hydrocephalus | Case Report - Pediatric Neurosurgery

Non-communicating hydrocephalus with a primary empty sella presenting with growth hormone deficiency and delayed puberty successfully treated by endoscopic third ventriculocisternostomy

Authors: Tomáš Krejčí, Ondřej Krejčí, Michael Mrůzek, Ivana Röschlová, Radim Lipina

Published in: Acta Neurochirurgica | Issue 2/2021

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Abstract

The authors present the unusual case of a 15-year-old boy with a primary empty sella caused by non-communicating hydrocephalus due to fourth ventricle outflow obstruction whose secondary symptoms of growth hormone deficiency and delayed puberty were successfully treated by endoscopic third ventriculocisternostomy (ETV). Hypopituitarism occurs only rarely in cases of hydrocephalus; rarer still are cases where hypopituitarism is the sole symptom of hydrocephalus. A primary empty sella may indicate elevated intracranial pressure; if the cause is non-communicating hydrocephalus, ETV is indicated as the preferred treatment modality.
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Metadata
Title
Non-communicating hydrocephalus with a primary empty sella presenting with growth hormone deficiency and delayed puberty successfully treated by endoscopic third ventriculocisternostomy
Authors
Tomáš Krejčí
Ondřej Krejčí
Michael Mrůzek
Ivana Röschlová
Radim Lipina
Publication date
01-02-2021
Publisher
Springer Vienna
Published in
Acta Neurochirurgica / Issue 2/2021
Print ISSN: 0001-6268
Electronic ISSN: 0942-0940
DOI
https://doi.org/10.1007/s00701-020-04481-9

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