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Published in: Surgery Today 11/2012

01-11-2012 | Case Report

Acute malignant intestinal obstruction accompanied by synchronous multifocal intestinal cancer in Peutz–Jeghers syndrome: report of a case

Authors: Tunc Eren, Baris Bayraktar, Yahya Celik, Salih Boluk, Gupse Adali

Published in: Surgery Today | Issue 11/2012

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Abstract

Acute mechanical intestinal obstruction is one of the most common modes of presentation in patients with Peutz–Jeghers syndrome (PJS). This report presents a case of PJS with malignant acute jejunal obstruction accompanied by synchronous foci of duodenal, jejunal, and ileal cancer originated from hamartomatous polyps. The follow-up endoscopic findings of the patient also revealed severe polyposis of the entire gastrointestinal tract, including the stomach and colon, in addition to the small intestine. Very few cases of multifocal synchronous small intestinal cancer in PJS patients have been reported in the previous literature.
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Metadata
Title
Acute malignant intestinal obstruction accompanied by synchronous multifocal intestinal cancer in Peutz–Jeghers syndrome: report of a case
Authors
Tunc Eren
Baris Bayraktar
Yahya Celik
Salih Boluk
Gupse Adali
Publication date
01-11-2012
Publisher
Springer Japan
Published in
Surgery Today / Issue 11/2012
Print ISSN: 0941-1291
Electronic ISSN: 1436-2813
DOI
https://doi.org/10.1007/s00595-012-0165-1

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