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01-08-2010 | Clinical Report

Anesthetic management for foramen magnum decompression in a patient with Morquio syndrome: a case report

Authors: Lakshminarsimhaiah Geetha, Muthuchellappan Radhakrishnan, Biligiri Sridhar Raghavendra, G. S. Umamaheswara Rao, Bhagavatula Indira Devi

Published in: Journal of Anesthesia | Issue 4/2010

Abstract

Morquio syndrome is a hereditary mucopolysaccharide disorder presenting with an abnormality of the craniocervical junction from childhood. We describe an adult patient who presented with Morquio syndrome who had subglottic narrowing of the airway, restrictive pulmonary disease, and mild mitral regurgitation and trivial aortic regurgitation. The anesthetic management of this patient for atlantoaxial stabilization is presented.

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Title: Anesthetic management for foramen magnum decompression in a patient with Morquio syndrome: a case report
Authors: Lakshminarsimhaiah Geetha
Muthuchellappan Radhakrishnan
Biligiri Sridhar Raghavendra
G. S. Umamaheswara Rao
Bhagavatula Indira Devi
Publication date: 01-08-2010
Publisher: Springer Japan
Published in: Journal of Anesthesia / Issue 4/2010
Print ISSN: 0913-8668
Electronic ISSN: 1438-8359
DOI: https://doi.org/10.1007/s00540-010-0963-9

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Anesthetic management for foramen magnum decompression in a patient with Morquio syndrome: a case report

Abstract

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Springer Medicine

Abstract

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