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Pediatric Nephrology
Published in: Pediatric Nephrology 2/2013

01-02-2013 | Review

Renovascular hypertension—is it fibromuscular dysplasia or Takayasu arteritis

Author: Kjell Tullus

Published in: Pediatric Nephrology | Issue 2/2013

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Abstract

Renovascular hypertension (RVH) can be caused by many different diseases, with the most common being fibromuscular dysplasia (FMD) and Takayasu arteritis (TA). A strikingly different diagnostic pattern is seen in children with RVH from different parts of the world. In Europe and North America, these children are mainly diagnosed as having FMD while in Asia and South Africa they will most often get a diagnosis of TA. When comparing the clinical diagnosis for FMD and TA, it becomes obvious that there is a great deal of overlap between the definitions of these two conditions. Different ways to come to the most accurate diagnosis using imaging of the blood vessel wall and positron emission tomography (PET) will be discussed. How an accurate diagnosis should influence the treatment of the children with these conditions will also be addressed.
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Metadata
Title
Renovascular hypertension—is it fibromuscular dysplasia or Takayasu arteritis
Author
Kjell Tullus
Publication date
01-02-2013
Publisher
Springer-Verlag
Published in
Pediatric Nephrology / Issue 2/2013
Print ISSN: 0931-041X
Electronic ISSN: 1432-198X
DOI
https://doi.org/10.1007/s00467-012-2151-7

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