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Pediatric Nephrology
Published in: Pediatric Nephrology 9/2006

01-09-2006 | Brief Report

Nephrogenic fibrosing dermopathy in children

Authors: Ari Auron, Lei Shao, Bradley A. Warady

Published in: Pediatric Nephrology | Issue 9/2006

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Abstract

Nephrogenic fibrosing dermopathy (NFD) is an entity of unknown etiology that has only been reported in patients with impaired kidney function. It has characteristic diagnostic findings by skin biopsy and due to its systemic involvement in some reported cases, the term “nephrogenic systemic fibrosis” has been recently suggested as more appropriate for the nomenclature of this entity. There is no curative treatment currently available and very few cases have been reported in children. We hereby report two cases so as to alert pediatric health care providers about the existence of this disorder.
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Metadata
Title
Nephrogenic fibrosing dermopathy in children
Authors
Ari Auron
Lei Shao
Bradley A. Warady
Publication date
01-09-2006
Publisher
Springer-Verlag
Published in
Pediatric Nephrology / Issue 9/2006
Print ISSN: 0931-041X
Electronic ISSN: 1432-198X
DOI
https://doi.org/10.1007/s00467-006-0174-7

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