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Published in:

01-02-2012 | Original Paper

Clinical features of congenital portosystemic shunt in children

Authors: Myung Jin Kim, Jae Sung Ko, Jeong Kee Seo, Hye Ran Yang, Ju Young Chang, Gi Beom Kim, Jung-Eun Cheon, Woo Sun Kim

Published in: European Journal of Pediatrics | Issue 2/2012

Abstract

Clinical features, images, complications, treatments, and prognosis of 10 children with congenital portosystemic shunt (CPSS) were reviewed. Nine children were diagnosed with intrahepatic shunts while one presented with extrahepatic shunt. CPSS was detected by prenatal ultrasonography in four infants. Three infants presented with galactosemia without an enzyme deficiency. Two children presented with mental retardation and attention deficit hyperactivity disorder. Pulmonary hypertension developed in two patients. Spontaneous closure occurred in four infants with intrahepatic shunts including patent ductus venosus. The shunts were closed using transcatheter embolizations in four patients with intrahepatic shunts. Conclusion: Intrahepatic shunts may close spontaneously. Transcatheter embolization is effective for the treatment of symptomatic intrahepatic shunts.

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Title: Clinical features of congenital portosystemic shunt in children
Authors: Myung Jin Kim
Jae Sung Ko
Jeong Kee Seo
Hye Ran Yang
Ju Young Chang
Gi Beom Kim
Jung-Eun Cheon
Woo Sun Kim
Publication date: 01-02-2012
Publisher: Springer-Verlag
Published in: European Journal of Pediatrics / Issue 2/2012
Print ISSN: 0340-6199
Electronic ISSN: 1432-1076
DOI: https://doi.org/10.1007/s00431-011-1564-9

At a glance: The STEP trials

Springer Medicine

Clinical features of congenital portosystemic shunt in children

Abstract

At a glance: The STEP trials

Springer Medicine

Abstract

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