Skip to main content
Top
Published in: European Journal of Pediatrics 9/2009

01-09-2009 | Short Report

Imaging of primary unilateral pulmonary hypoplasia: a case report

Authors: P. Demaret, R. Menten, C. Debauche, S. Moniotte

Published in: European Journal of Pediatrics | Issue 9/2009

Login to get access

Abstract

Background

Pulmonary hypoplasia is a rare cause of neonatal dyspnea almost always secondary to other conditions. We report an exceedingly rare case of primary unilateral pulmonary hypoplasia.

Results and discussion

This case illustrates the role of prenatal magnetic resonance imaging when this condition is suspected during the fetal life. Combined with ultrasounds, this imaging modality offers a three-dimensional evaluation of the lungs that can be critical for postnatal medical management.
Literature
1.
go back to reference Abrams ME, Ackerman VL, Engle WA (2004) Primary unilateral pulmonary hypoplasia: neonate through early childhood—case report, radiographic diagnosis and review of the literature. J Perinatol 24(10):667–670PubMedCrossRef Abrams ME, Ackerman VL, Engle WA (2004) Primary unilateral pulmonary hypoplasia: neonate through early childhood—case report, radiographic diagnosis and review of the literature. J Perinatol 24(10):667–670PubMedCrossRef
2.
go back to reference Chou AK, Huang SC, Chen SJ et al (2007) Unilateral lung agenesis—detrimental roles of surrounding vessels. Pediatr Pulmonol 42(3):242–248PubMedCrossRef Chou AK, Huang SC, Chen SJ et al (2007) Unilateral lung agenesis—detrimental roles of surrounding vessels. Pediatr Pulmonol 42(3):242–248PubMedCrossRef
3.
go back to reference Frey B, Fleishauer A, Gersbach M (1994) Familial isolated pulmonary hypoplasia: a case report, suggesting autosomal recessive inheritance. Eur J Pediatr 153:460–463PubMedCrossRef Frey B, Fleishauer A, Gersbach M (1994) Familial isolated pulmonary hypoplasia: a case report, suggesting autosomal recessive inheritance. Eur J Pediatr 153:460–463PubMedCrossRef
4.
go back to reference Green RA, Shaw DG, Haworth SG (1999) Familial pulmonary hypoplasia: plain film appearances with histopathological correlation. Pediatr Radiol 29:455–458PubMedCrossRef Green RA, Shaw DG, Haworth SG (1999) Familial pulmonary hypoplasia: plain film appearances with histopathological correlation. Pediatr Radiol 29:455–458PubMedCrossRef
5.
go back to reference Langer R, Kaufmann HJ (1986) Primary (isolated) bilateral pulmonary hypoplasia: a comparative study of radiologic findings and autopsy results. Pediatr Radiol 16:175–179PubMedCrossRef Langer R, Kaufmann HJ (1986) Primary (isolated) bilateral pulmonary hypoplasia: a comparative study of radiologic findings and autopsy results. Pediatr Radiol 16:175–179PubMedCrossRef
6.
go back to reference Mendelsohn G, Hutchins GM (1971) Primary pulmonary hypoplasia. Report of a case with polyhydramnios. Am J Dis Child 131:1220–1223 Mendelsohn G, Hutchins GM (1971) Primary pulmonary hypoplasia. Report of a case with polyhydramnios. Am J Dis Child 131:1220–1223
7.
go back to reference Moerman P, Vanhole C, Devlieger H, Fryns J (1998) Severe primary pulmonary hypoplasia (‘acinar dysplasia’) in sibs: a genetically determined mesodermal defect. J Med Genet 35:964–965PubMedCrossRef Moerman P, Vanhole C, Devlieger H, Fryns J (1998) Severe primary pulmonary hypoplasia (‘acinar dysplasia’) in sibs: a genetically determined mesodermal defect. J Med Genet 35:964–965PubMedCrossRef
8.
go back to reference Odd DE, Battin MR, Hallam L, Knight DB (2003) Primary pulmonary hypoplasia: a case report and review of the literature. J Paediatr Child Health 39(6):467–469PubMedCrossRef Odd DE, Battin MR, Hallam L, Knight DB (2003) Primary pulmonary hypoplasia: a case report and review of the literature. J Paediatr Child Health 39(6):467–469PubMedCrossRef
9.
go back to reference Swischuk LE, Richardson CJ, Nichols MM, Ingman MJ (1979) Primary pulmonary hypoplasia in the neonate. J Pediatr 95:573–577PubMedCrossRef Swischuk LE, Richardson CJ, Nichols MM, Ingman MJ (1979) Primary pulmonary hypoplasia in the neonate. J Pediatr 95:573–577PubMedCrossRef
Metadata
Title
Imaging of primary unilateral pulmonary hypoplasia: a case report
Authors
P. Demaret
R. Menten
C. Debauche
S. Moniotte
Publication date
01-09-2009
Publisher
Springer-Verlag
Published in
European Journal of Pediatrics / Issue 9/2009
Print ISSN: 0340-6199
Electronic ISSN: 1432-1076
DOI
https://doi.org/10.1007/s00431-008-0893-9

Other articles of this Issue 9/2009

European Journal of Pediatrics 9/2009 Go to the issue