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European Archives of Oto-Rhino-Laryngology

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01-12-2007 | Case Report

Total hearing loss and blindness caused by relapsing polychondritis and myelodysplastic syndrome

Authors: Bozena Coha, Ljubica Fustar-Preradovic, Sandra Sekelj, Alen Sekelj

Published in: European Archives of Oto-Rhino-Laryngology | Issue 12/2007

Abstract

Relapsing polychondritis is an autoimmune disease that primarily manifests as cartilaginous tissue destruction. However, the immune impairment may also involve noncartilaginous tissues such as kidneys, blood vessels, etc. The disease may occur as a primary disorder or in association with other diseases. The case of a female patient with concurrent manifestation of myelodysplastic syndrome—refractory anemia with excess blasts, and relapsing polychondritis, is presented. The diagnosis of relapsing polychondritis was established ten months after the diagnosis of myelodysplastic syndrome, when the criteria for the former were met. Total hearing loss and blindness developed soon thereafter.

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Title: Total hearing loss and blindness caused by relapsing polychondritis and myelodysplastic syndrome
Authors: Bozena Coha
Ljubica Fustar-Preradovic
Sandra Sekelj
Alen Sekelj
Publication date: 01-12-2007
Publisher: Springer-Verlag
Published in: European Archives of Oto-Rhino-Laryngology / Issue 12/2007
Print ISSN: 0937-4477
Electronic ISSN: 1434-4726
DOI: https://doi.org/10.1007/s00405-007-0387-9

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Springer Medicine

Total hearing loss and blindness caused by relapsing polychondritis and myelodysplastic syndrome

Abstract

At a glance: The STEP trials

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Abstract

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