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01-07-2016 | Case Report

Presentation and management of pulmonary sequestration with total visceral inflow and outflow

Authors: Christopher L. Sudduth, Sarah J. Hill, Mehul V. Raval

Published in: Pediatric Surgery International | Issue 7/2016

Abstract

Two of the most common types of congenital thoracic malformations are congenital pulmonary airway malformations (CPAMs) and bronchopulmonary sequestrations (BPS). Here we present the first known case of a hybrid lesion, with coexisting features of an extralobar sequestration (ELS) and CPAM type 2, with arterial inflow from the celiac trunk and venous outflow to the portal vein. The clinical presentation, investigative imaging and timing of surgery are discussed.

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Title: Presentation and management of pulmonary sequestration with total visceral inflow and outflow
Authors: Christopher L. Sudduth
Sarah J. Hill
Mehul V. Raval
Publication date: 01-07-2016
Publisher: Springer Berlin Heidelberg
Published in: Pediatric Surgery International / Issue 7/2016
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI: https://doi.org/10.1007/s00383-016-3882-5

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