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Published in: Pediatric Surgery International 12/2011

01-12-2011 | Original Article

Pseudopapillary tumor in pediatric age: clinical and surgical management

Authors: Nicola Zampieri, Nicola Schiavo, Paola Capelli, Aldo Scarpa, Claudio Bassi, Francesco Saverio Camoglio

Published in: Pediatric Surgery International | Issue 12/2011

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Abstract

Background

Solid pseudopapillary tumors of the pancreas are rare exocrine pancreatic tumors. Through a review of pediatric cases in a single Institution, we present the clinical and surgical management of this neoplasm.

Methods

We retrospectively reviewed the clinical charts of patients treated at our unit between 1995 and 2009 for SPT. Clinical and surgical management were analyzed and reported.

Results

During the study period 11 patients underwent surgery for pseudopapillary tumor. Five patients were treated with duodenum-preserving pancreatic head resection and six patients with splenopancreasectomy with a Roux-en-Y pancreatic jejunostomy. Patients did not show recurrence and are currently disease free. Blood tests, Ultrasound, Computed tomography and Magnetic Resonance Imaging were not useful to preoperatively identify the nature of the pancreatic masses.

Conclusion

Solid pseudopapillary tumor is a rare condition that should be taken into account for the differential diagnosis of pancreatic masses in pediatric age. Due to its favourable prognosis, surgical removal should be planned and done following the intraoperative findings.
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Metadata
Title
Pseudopapillary tumor in pediatric age: clinical and surgical management
Authors
Nicola Zampieri
Nicola Schiavo
Paola Capelli
Aldo Scarpa
Claudio Bassi
Francesco Saverio Camoglio
Publication date
01-12-2011
Publisher
Springer-Verlag
Published in
Pediatric Surgery International / Issue 12/2011
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI
https://doi.org/10.1007/s00383-011-2947-8

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