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Pediatric Surgery International
Published in: Pediatric Surgery International 6/2008

01-06-2008 | Review Article

Congenital cystic lung disease: contemporary antenatal and postnatal management

Authors: Richard G. Azizkhan, Timothy M. Crombleholme

Published in: Pediatric Surgery International | Issue 6/2008

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Abstract

Congenital cystic lung disease comprises a broad spectrum of rare but clinically significant developmental abnormalities, including congenital pulmonary adenomatoid malformations, bronchopulmonary sequestrations, bronchogenic cysts, and congenital lobar emphysema that result from perturbations in lung and airway embryogenesis. As congenital lung lesions are now more commonly recognized antenatally, mothers require accurate prenatal counseling and appropriate perinatal management. In light of long-term complications of infection and malignancy, there is growing consensus that infants with asymptomatic lesions should undergo elective excision of congenital pulmonary adenomatoid malformation (CPAM) or bronchopulmonary sequestration (BPS). This review will focus on advancements and current practice in the diagnosis and management of CPAM and BPS, identifying aspects of the literature that are confusing or controversial. Although our knowledge and pre- and postnatal management of lung lesions will continue to evolve and improve, there is a compelling need for a unified clinical and pathological classification system that creates a common platform for discussion, clinical management, and research.
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Metadata
Title
Congenital cystic lung disease: contemporary antenatal and postnatal management
Authors
Richard G. Azizkhan
Timothy M. Crombleholme
Publication date
01-06-2008
Publisher
Springer-Verlag
Published in
Pediatric Surgery International / Issue 6/2008
Print ISSN: 0179-0358
Electronic ISSN: 1437-9813
DOI
https://doi.org/10.1007/s00383-008-2139-3

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