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Child's Nervous System
Published in: Child's Nervous System 9/2020

01-09-2020 | Bone Defect | Technical Note

Preoperative planning with a 3D model and repair of sphenoid dysplasia: a technical note

Authors: Peter Spazzapan, Miha Verdenik, Andreja Eberlinc

Published in: Child's Nervous System | Issue 9/2020

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Abstract

Introduction

Sphenoid dysplasia is a distinctive marker of neurofibromatosis 1. It is a malformation of the sphenoid bone characterized by an enlargement of the superior orbital fissure, through which the intracranial content herniates, leading to a facial disfigurement and exophthalmos and to a potential visual deterioration. Surgical treatment has the aim of separating the intracranial from the intraorbital space.

Methods and results

We present a new technique for the repair of sphenoid dysplasia, based on the preoperative planning on a 3D print of the skull base.

Conclusions

The use of a 3D skull base model allows an effective surgical planning and a precise modelling of the titanium mesh, which is implanted to separate the intracranial from the intraorbital space.
Literature
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Arrington DK, Danehy AR, Peleggi A, Proctor MR, Irons MB, Ullrich NJ (2013) Calvarial defects and skeletal dysplasia in patients with neurofibromatosis type 1. J Neurosurg Pediatr 11:410–416CrossRef
2.
Di Rocco C, Samii A, Tamburrini G, Massimi L, Giordano M (2017) Sphenoid dysplasia in neurofibromatosis type 1: a new technique for repair. Childs Nerv Syst 33:983–986CrossRef
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Niddam J, Bosc R, Suffee TM, Le Guerinel C, Wolkenstein P, Meningaud JP (2014) Treatment of sphenoid dysplasia with a titanium-reinforced porous polyethylene implant in orbitofrontal neurofibroma: report of three cases. J Craniomaxillofac Surg 42:1937–1941CrossRef
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Papay FA, Zins JE, Hahn JF (1996) Split calvarial bone graft in cranio-orbital sphenoid wing reconstruction. J Craniofac Surg 7:133–139CrossRef
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Wu CT, Lee ST, Chen JF, Lin KL, Yen SH (2008) Computer-aided design for three-dimensional titanium mesh used for repairing skull base bone defect in pediatric neurofibromatosis type 1. A novel approach combining biomodeling and neuronavigation. Pediatr Neurosurg 44:133–139CrossRef
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Friedrich RE, Heiland M, Kehler U, Schmelzle R et al (2003) Reconstruction of sphenoid wing dysplasia with pulsating exophthalmos in a case of neurofibromatosis type 1 supported by intraoperative navigation using a new skull reference system. Skull base 13:211–217CrossRef
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Coelho G, Chaves TMF, Goes AF, Del Massa EC, Moraes O, Yoshida M (2018) Multimaterial 3D printing preoperative planning for frontoethmoidal meningoencephalocele surgery. Childs Nerv Syst 34:749–756CrossRef
Metadata
Title
Preoperative planning with a 3D model and repair of sphenoid dysplasia: a technical note
Authors
Peter Spazzapan
Miha Verdenik
Andreja Eberlinc
Publication date
01-09-2020
Publisher
Springer Berlin Heidelberg
Published in
Child's Nervous System / Issue 9/2020
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-020-04759-4

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