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01-05-2019 | Case Report

Surgical consideration in Hunter syndrome: a case of hydrocephalus and a case of epidural hematoma

Authors: Jin Li, Xinyan Zhang, Raynald, Tao Jiang, Chunde Li

Published in: Child's Nervous System | Issue 5/2019

Abstract

Introduction

Hunter syndrome (HS) is a rare X-linked lysosomal storage disorder which affects multiple organ systems. Surgical intervention and general anesthesia should be used with caution because of significant airway complications.

Case report

Two HS patients underwent surgery with different prognosis are presented below. In the first case, symptoms of progressive disabilities on motor function, language, intelligence, and development last for 1 year in a 6-year-old boy; magnetic resonance imaging (MRI) showed severe hydrocephalus. Third ventriculostomy was performed in this patient to relieve the hydrocephalus. Unfortunately, this patient died postoperatively due to postsurgical tracheal collapse. In the second case, an 8-year-old girl was referred to our hospital with epidural hematoma because of a falling accident. Trephination surgery was performed under local anesthesia to remove the hematoma. Three days postsurgical, the patient was discharged uneventfully.

Conclusion

General anesthesia in HS patients was associated with poor prognosis due to respiratory complications. Local anesthesia and less intensified treatment should be recommended.

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Title: Surgical consideration in Hunter syndrome: a case of hydrocephalus and a case of epidural hematoma
Authors: Jin Li
Xinyan Zhang
Raynald
Tao Jiang
Chunde Li
Publication date: 01-05-2019
Publisher: Springer Berlin Heidelberg
Published in: Child's Nervous System / Issue 5/2019
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-018-3998-0

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Surgical consideration in Hunter syndrome: a case of hydrocephalus and a case of epidural hematoma

Abstract

Introduction

Case report

Conclusion

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Abstract

Introduction

Case report

Conclusion

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