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Child's Nervous System

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01-02-2019 | Case Report

Primitive myxoid mesenchymal tumor of infancy with brain metastasis: first reported case

Authors: Amna Afzal Saeed, Quratulain Riaz, Nasir Ud Din, Sadaf Altaf

Published in: Child's Nervous System | Issue 2/2019

Abstract

Introduction

Primitive myxoid mesenchymal tumor of infancy (PMMTI) is a recently diagnosed entity, with only a handful of cases reported to date.

Case description

Herein, we present the occurrence of this tumor in a 2-year-old boy, initially diagnosed as primitive neuroectodermal tumor of the extremity and treated with chemotherapy and surgical resection. He later presented with a cerebellar lesion, and biopsy was consistent with PMMTI.

Conclusion

While there have been previous cases of PMMTI reported with loco-regional metastatic spread, to our knowledge, there is no known incidence of distant metastasis with involvement of the central nervous system, which makes this case the first of its kind.

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Title: Primitive myxoid mesenchymal tumor of infancy with brain metastasis: first reported case
Authors: Amna Afzal Saeed
Quratulain Riaz
Nasir Ud Din
Sadaf Altaf
Publication date: 01-02-2019
Publisher: Springer Berlin Heidelberg
Published in: Child's Nervous System / Issue 2/2019
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-018-3964-x

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Primitive myxoid mesenchymal tumor of infancy with brain metastasis: first reported case

Abstract

Introduction

Case description

Conclusion

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Abstract

Introduction

Case description

Conclusion

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