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01-04-2018 | Case Report

Management of idiopathic spinal epidural lipomatosis: a case report and review of the literature

Authors: Steven T. Papastefan, Abhiraj D. Bhimani, Steven Denyer, Sajeel R. Khan, Darian R. Esfahani, Demetrios C. Nikas, Ankit I. Mehta

Published in: Child's Nervous System | Issue 4/2018

Abstract

Background

Spinal epidural lipomatosis (SEL) is a rare pathologic growth of histologically normal unencapsulated adipose tissue in the epidural space. Although rare, SEL can compress the spinal cord or nerve roots causing myelopathy or radiculopathy. While SEL has been associated with long-term exposure to endogenous or exogenous steroids and obesity, idiopathic forms of SEL are much rarer.

Case report

In this report, we present the first case of SEL isolated to the cervical region compressing the spinal cord in a healthy, non-obese, preadolescent patient.

Conclusion

Idiopathic SEL in the pediatric population is a rare entity. This is the first case of epidural lipomatosis isolated to the cervical region in an adult or child patient. In refractory, symptomatic cases of idiopathic SEL, surgical decompression is often required.

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Title: Management of idiopathic spinal epidural lipomatosis: a case report and review of the literature
Authors: Steven T. Papastefan
Abhiraj D. Bhimani
Steven Denyer
Sajeel R. Khan
Darian R. Esfahani
Demetrios C. Nikas
Ankit I. Mehta
Publication date: 01-04-2018
Publisher: Springer Berlin Heidelberg
Published in: Child's Nervous System / Issue 4/2018
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-017-3706-5

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Management of idiopathic spinal epidural lipomatosis: a case report and review of the literature

Abstract

Background

Case report

Conclusion

At a glance: The ONWARDS insulin icodec trials

Springer Medicine

Abstract

Background

Case report

Conclusion

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