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Child's Nervous System
Published in: Child's Nervous System 9/2017

01-09-2017 | Case Report

Management of an unusual, recurrent neurenteric cyst in an infant: case report and review of the literature

Authors: Darian R. Esfahani, Laura Burokas, Henry G. Brown, Yoon S. Hahn, Dimitrios Nikas

Published in: Child's Nervous System | Issue 9/2017

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Abstract

Purpose

Neurenteric cysts are rare congenital remnants formed by a failure of separation between endoderm and ectoderm in utero.

Methods

We describe a case of a 7-month-old male with a large cervical neurenteric cyst presenting with intermittent neck stiffness and irritability.

Results

This cyst was resected, recurred, and required repeat surgery. The patient’s postoperative course included aseptic meningitis and hydrocephalus requiring ventriculoperitoneal shunt and later management of tethered cord, necessitating detethering.

Conclusion

Unique features of this case include the presence of intermittent pain symptoms, which may be attributable to cyst filling and emptying. Hydrocephalus is an uncommon finding that may be secondary to aseptic meningitis from cyst rupture. Tethered cord is also an unusual entity that can accompany this diagnosis, warranting additional imaging work-up and monitoring.
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Metadata
Title
Management of an unusual, recurrent neurenteric cyst in an infant: case report and review of the literature
Authors
Darian R. Esfahani
Laura Burokas
Henry G. Brown
Yoon S. Hahn
Dimitrios Nikas
Publication date
01-09-2017
Publisher
Springer Berlin Heidelberg
Published in
Child's Nervous System / Issue 9/2017
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-017-3487-x

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