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Child's Nervous System

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01-11-2016 | Case Report

Glial heterotopia of the orbit: a rare cause of proptosis

Authors: Souad Bakhti, Fella Terkmani, Nabila Tighilt, Youcef Benmouma, Nazim Boumehdi, Mohamed Djennas

Published in: Child's Nervous System | Issue 11/2016

Abstract

Background

Glial heterotopia is defined as presence of normal glial tissue in an unusual location without connection with the brain. It is a very rare clinical entity occuring mostly in the head and neck region which is generally present at birth. Orbital location is very rare.

Case Report

We report a case of a 4-month-old girl presenting congenital proptosis with progressive increase. CT scan revealed an intraorbital mass without bony defect. The patient was operated, and resection was subtotal. Histologically, the tumor was composed of glial tissue with plexus choroid and pathologist concluded glial heterotopia. The child is under constant medical supervision because recurrences can be observed after incomplete resection; she had no new clinical signs at 18 months follow-up.

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Title: Glial heterotopia of the orbit: a rare cause of proptosis
Authors: Souad Bakhti
Fella Terkmani
Nabila Tighilt
Youcef Benmouma
Nazim Boumehdi
Mohamed Djennas
Publication date: 01-11-2016
Publisher: Springer Berlin Heidelberg
Published in: Child's Nervous System / Issue 11/2016
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-016-3107-1

At a glance: The STEP trials

Springer Medicine

Glial heterotopia of the orbit: a rare cause of proptosis

Abstract

Background

Case Report

At a glance: The STEP trials

Springer Medicine

Abstract

Background

Case Report

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