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Child's Nervous System
Published in: Child's Nervous System 11/2009

01-11-2009 | Original Paper

Transsphenoidal meningoencephalocele associated with cleft lip and palate: challenges for diagnosis and surgical treatment

Authors: Diogo Franco, Nivaldo Alonso, Renata Ruas, Renato da Silva Freitas, Talita Franco

Published in: Child's Nervous System | Issue 11/2009

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Abstract

Purpose

The aim of this study was to highlight the challenges for early diagnosis and the difficulties observed in surgical treatment of patients with transsphenoidal meningoencephalocele associated with cleft lip and/or palate.

Method

We evaluated six male patients treated over the course of 4 years. Five patients presented encephalic herniation with nonfunctional brain tissue; one of these presented herniation of the pituitary gland and cerebral ventricles.

Results

All the patients received surgical treatment for the cleft lip and/or palate. Only one patient underwent repair of the meningoencephalocele, via nasal endoscopy. There were no postprocedural clinical or surgical complications.

Conclusion

The tendency is to avoid neurosurgery, opting for periodic follow-up with magnetic resonance imaging. In the presence of cleft palate, palatoplasty is essential to protect the meningoencephalocele.
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Metadata
Title
Transsphenoidal meningoencephalocele associated with cleft lip and palate: challenges for diagnosis and surgical treatment
Authors
Diogo Franco
Nivaldo Alonso
Renata Ruas
Renato da Silva Freitas
Talita Franco
Publication date
01-11-2009
Publisher
Springer-Verlag
Published in
Child's Nervous System / Issue 11/2009
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-009-0918-3

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