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Child's Nervous System
Published in: Child's Nervous System 8/2009

01-08-2009 | Case for Discussion

Spinal epidural hematoma in hemophilic children: controversies in management

Authors: Pilar Varela Rois, Manuel Rodríguez López, Beatriz Cabanas López de Vergara, Adolfo de la Lama Zaragoza, Jesús González García, Jorge Mañas Uxo

Published in: Child's Nervous System | Issue 8/2009

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Abstract

Introduction and objective

Spinal epidural hematoma (SEH) is an uncommon complication in hemophilic children. It can produce rapidly progressive neurological deficits. We aim to discuss the different management options for these patients.

Case report

A 13-year-old boy with a history of hemophilia A was admitted with acute onset of localized spine pain and weakness. No trauma was reported on review of the history. Recombinant factor VIII aggressive replacement therapy was started. Spinal magnetic resonance imaging revealed an extradural mass lesion extending from D5 to D6 level. Emergency hemilaminectomies of D5 and D6 and evacuation of the clot were done. The patient made excellent recovery following surgery.

Conclusion

Early diagnosis and immediate aggressive replacement therapy are mandatory in the management of SEH. Prompt surgical decompression to avoid any permanent neurological deficit is a safe and effective treatment option for an SEH in selected hemophilic children.
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Metadata
Title
Spinal epidural hematoma in hemophilic children: controversies in management
Authors
Pilar Varela Rois
Manuel Rodríguez López
Beatriz Cabanas López de Vergara
Adolfo de la Lama Zaragoza
Jesús González García
Jorge Mañas Uxo
Publication date
01-08-2009
Publisher
Springer-Verlag
Published in
Child's Nervous System / Issue 8/2009
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-009-0861-3

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