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Child's Nervous System

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01-08-2009 | Case Report

Primary intracranial leiomyosarcoma: a case report and review of the literature

Authors: C. S. Mathieson, E. J. St George, W. Stewart, J. Sastry, S. Jamal

Published in: Child's Nervous System | Issue 8/2009

Abstract

Introduction

Malignant tumours of the central nervous system (CNS) represent the second most common cancer type in the paediatric population of developed countries, and mortality caused by CNS tumours is the highest among paediatric cancers. Tumours of mesenchymal origin occurring either as primary or secondary lesions of the central nervous system are very rare in children. This paper describes the case of a 5-year-old non-immunocompromised male who presented with a right frontal primary intracranial leiomyosarcoma associated with large subdural collections.

Discussion and conclusion

Following surgical excision and adjuvant chemoradiotherapy, the patient has remained disease-free for 18 months. The literature is reviewed and the possible association of the chronic subdurals to the later development of the leiomyosarcoma explored.

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Title: Primary intracranial leiomyosarcoma: a case report and review of the literature
Authors: C. S. Mathieson
E. J. St George
W. Stewart
J. Sastry
S. Jamal
Publication date: 01-08-2009
Publisher: Springer-Verlag
Published in: Child's Nervous System / Issue 8/2009
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-009-0845-3

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Primary intracranial leiomyosarcoma: a case report and review of the literature

Abstract

Introduction

Discussion and conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Introduction

Discussion and conclusion

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