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CardioVascular and Interventional Radiology
Published in: CardioVascular and Interventional Radiology 1/2008

01-01-2008 | Case Report

Endovascular Treatment of a Carotid Dissecting Pseudoaneurysm in a Patient with Ehlers-Danlos Syndrome Type IV with Fatal Outcome

Authors: Siok Ping Lim, Martin J. Duddy

Published in: CardioVascular and Interventional Radiology | Issue 1/2008

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Abstract

We present a patient with Ehlers-Danlos syndrome type IV (EDS IV) with a carotid dissecting pseudoaneurysm causing severe carotid stenosis. This lesion was treated endovascularly. Unfortunately, the patient died of remote vascular catastrophes (intracranial hemorrhage and abdominal aortic rupture). This unique case illustrates the perils of endovascular treatment of EDS IV patients and the need for preoperative screening for concomitant lesions. It also shows that a dissecting pseudoaneurysm can feasibly be treated with a covered stent and that closure is effective using Angioseal in patients with EDS IV.
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Metadata
Title
Endovascular Treatment of a Carotid Dissecting Pseudoaneurysm in a Patient with Ehlers-Danlos Syndrome Type IV with Fatal Outcome
Authors
Siok Ping Lim
Martin J. Duddy
Publication date
01-01-2008
Publisher
Springer-Verlag
Published in
CardioVascular and Interventional Radiology / Issue 1/2008
Print ISSN: 0174-1551
Electronic ISSN: 1432-086X
DOI
https://doi.org/10.1007/s00270-007-9135-1

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