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Skeletal Radiology
Published in: Skeletal Radiology 4/2018

01-04-2018 | Case Report

Parosteal extra-axial chordoma of the second metacarpal bone: a case report with literature review

Authors: Shinji Tsukamoto, Daniel Vanel, Alberto Righi, Davide Maria Donati, Costantino Errani

Published in: Skeletal Radiology | Issue 4/2018

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Abstract

Extra-axial chordoma is a chordoma that occurs in non-axial locations. It is a very rare tumor, with 20 cases reported to date; 14 in bone and six in soft tissue. Of the 14 skeletal extra-axial chordomas, ten were intramedullary and four were intracortical. We report the first case of parosteal extra-axial chordoma arising in the second metacarpal bone, expressing brachyury on immunohistochemical analysis, and describe the pathologic and radiologic findings. We suggest that extra-axial chordoma can occur in parosteal bone lesions or the hand, without features of bone distribution or bone-specific sites.
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Metadata
Title
Parosteal extra-axial chordoma of the second metacarpal bone: a case report with literature review
Authors
Shinji Tsukamoto
Daniel Vanel
Alberto Righi
Davide Maria Donati
Costantino Errani
Publication date
01-04-2018
Publisher
Springer Berlin Heidelberg
Published in
Skeletal Radiology / Issue 4/2018
Print ISSN: 0364-2348
Electronic ISSN: 1432-2161
DOI
https://doi.org/10.1007/s00256-017-2818-z

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