Published in:
01-12-2011 | Test Yourself: Answer
Osteogenesis imperfecta type V
Authors:
Peter Kei Tat Hui, Joanna Y. L. Tung, Wendy W. M. Lam, M. T. Chau
Published in:
Skeletal Radiology
|
Issue 12/2011
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Excerpt
Osteogenesis imperfecta type V was first described in 2000. It is a distinct clinical entity with unique clinical, radiological, and histological features. Clinically, it is only moderately deforming. Patients have normal sclera and teeth. Radiological diagnostic criteria include a triad of calcification of the radioulnar interosseous membrane, presence of hypertrophic callus at fractures or post-operative sites, and radiodense metaphyseal band adjacent to growth plates [
1]. Histologically, it is distinguished by a mesh-like pattern of lamellation under polarized light microscopy for iliac bone samples. …
