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Published in: Pediatric Radiology 12/2013

01-12-2013 | Original Article

In utero magnetic resonance imaging for diagnosis of dural venous sinus ectasia with thrombosis in the fetus

Authors: Evgenia Maria Fanou, Mike J. Reeves, David T. Howe, Harriet Joy, Susan Morris, Sarah Russell, Paul D. Griffiths

Published in: Pediatric Radiology | Issue 12/2013

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Abstract

Background

Dural venous sinus ectasia with thrombosis (DVSET) in the fetus is a rare condition that can be diagnosed prenatally with the use of fetal MR imaging, yet with limited indication of long-term clinical significance.

Objective

To describe and evaluate the diagnostic value of fetal MR imaging in the prenatal diagnosis of dural venous sinus ectasia with thrombosis and its clinical significance.

Materials and methods

We report a series of nine fetuses with dural venous sinus ectasia with thrombosis. The mothers, located in four feto-maternal centres, were referred for fetal MR imaging due to space occupying lesions identified on second-trimester antenatal ultrasound.

Results

In all but one case the dural venous sinus ectasia with thrombosis was in the vicinity of the venous confluence (VC) with various extension in the posterior dural sinuses. Antenatal follow-up imaging was performed in seven cases and showed progression in one, stable appearances in one and regression in five cases. Three pregnancies were terminated. In the remaining six cases there was no reported neurological deficit at up to 44 months of clinical follow-up.

Conclusion

This is among the largest series of postnatal clinical follow-up in cases of prenatal diagnosis of dural venous sinus ectasia with thrombosis in the literature. Clinical follow-up suggests a good prognosis when antenatal follow-up shows partial or complete thrombus resolution.
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Metadata
Title
In utero magnetic resonance imaging for diagnosis of dural venous sinus ectasia with thrombosis in the fetus
Authors
Evgenia Maria Fanou
Mike J. Reeves
David T. Howe
Harriet Joy
Susan Morris
Sarah Russell
Paul D. Griffiths
Publication date
01-12-2013
Publisher
Springer Berlin Heidelberg
Published in
Pediatric Radiology / Issue 12/2013
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI
https://doi.org/10.1007/s00247-013-2745-7

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