Top

Published in:

01-09-2012 | Case Report

Multidetector CT of right-sided congenital diaphragmatic hernia associated with hepatopulmonary fusion in a newborn

Authors: Luc Breysem, Sophie Vanhaesebrouck, Marc Gewillig, Steven Dymarkowski, Maria-Helena Smet

Published in: Pediatric Radiology | Issue 9/2012

Abstract

We present a neonate with a complex congenital cardiopathy and a right-sided diaphragmatic hernia complicated with hepatopulmonary fusion. Radiography, abdominal US and multidetector CT (MDCT) demonstrated right-sided lung hypoplasia and liver herniation. In addition, MDCT angiography showed abnormal pulmonary vascular anatomy. At surgery, a right-sided diaphragmatic hernia with a partially herniated liver and hepatopulmonary fusion was confirmed. There was no aberrant systemic vascular supply towards the lower lobe, as seen in extralobar sequestration. MDCT angiography of the chest and upper abdomen with optimal enhancement and reconstruction of the pulmonary and hepatic vasculature can demonstrate associated anomalies in cases of suspected primary or secondary right lung hypoplasia.

Katz S, Kidron D, Litmanovitz I et al (1998) Fibrous fusion between the liver and the lung: an unusual complication of right congenital diaphragmatic hernia. J Pediatr Surg 33:766–767PubMedCrossRef

Slovis TL, Farmer DL, Berdon WE et al (2000) Hepatic pulmonary fusion in neonates. AJR 174:229–233PubMed

Keller RL, Aaroz PA, Hawgood S et al (2003) MR imaging of hepatic pulmonary fusion in neonates. AJR Am J Roentgenol 180:438–440PubMed

Donnelly LF, Sakurai M, Klosterman LA et al (1999) Correlation between findings on chest radiography and survival in neonates with congenital diaphragmatic hernia. AJR 173:1589–1593PubMed

Gander JW, Kadenhe-Chiweshe A, Fisher JC et al (2010) Hepatic pulmonary fusion in an infant with a right-sided congenital diaphragmatic hernia and contralateral mediastinal shift. J Pediatr Surg 45:265–268PubMedCrossRef

Abdullah MM, Lacro RV, Smallhorn J et al (2000) Fetal cardiac dextroposition in the absence of an intrathoracic mass: sign of significant right lung hypoplasia. J Ultrasound Med 19:669–676PubMed

Lee EY, Siegel MJ, Sierra LM et al (2004) Evaluation of angioarchitecture of pulmonary sequestration in pediatric patients using 3D MDCT angiography. AJR 183:183–188PubMed

Tanaka S, Kubota M, Yagi M et al (2006) Treatment of a case with right-sided diaphragmatic hernia associated with an abnormal vessel communication between a herniated liver and the right lung. J Pediatr Surg 41:e25–28PubMedCrossRef

Title: Multidetector CT of right-sided congenital diaphragmatic hernia associated with hepatopulmonary fusion in a newborn
Authors: Luc Breysem
Sophie Vanhaesebrouck
Marc Gewillig
Steven Dymarkowski
Maria-Helena Smet
Publication date: 01-09-2012
Publisher: Springer-Verlag
Published in: Pediatric Radiology / Issue 9/2012
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI: https://doi.org/10.1007/s00247-012-2379-1

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Multidetector CT of right-sided congenital diaphragmatic hernia associated with hepatopulmonary fusion in a newborn

Abstract

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Please log in to get access to this content

Other articles of this Issue 9/2012

Colloid cyst of the third ventricle associated with anterior cerebral artery trifurcation and agenesis of the corpus callosum: findings on MRI and CT angiography

Utilizing ultrasonography in the diagnosis of pediatric fibroepithelial polyps causing ureteropelvic junction obstruction

Digital radiography: optimization of image quality and dose using multi-frequency software

Diagnosis and subsequent US-guided percutaneous drainage of an adrenal abscess in a 5-week-old infant

Hermes

Contrast enema findings in patients presenting with poor functional outcome after primary repair for Hirschsprung disease