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01-09-2007 | Case Report

Spontaneous hemorrhage simulating rapid growth of a benign subperiosteal plexiform neurofibroma

Authors: Netta M. Blitman, Jeffrey M. Levsky, Esperanza Villanueva-Siles, Beverly A. Thornhill

Published in: Pediatric Radiology | Issue 9/2007

Abstract

Spontaneous subperiosteal hemorrhage is a rare complication of von Recklinghausen’s disease. There are few reports describing the MR imaging characteristics of this entity. Our case is unique among these as an underlying plexiform neurofibroma was visualized by MR imaging. We present a 12-year-old child with neurofibromatosis 1 who presented with a rapidly enlarging mass of the fibula. Surgery and pathology revealed subperiosteal hemorrhage into a benign, plexiform neurofibroma. The MR imaging features, pathogenesis and clinical implications of this entity are discussed. Recognition of this disease process and differentiating it from malignant transformation can prevent unnecessary surgery.

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Title: Spontaneous hemorrhage simulating rapid growth of a benign subperiosteal plexiform neurofibroma
Authors: Netta M. Blitman
Jeffrey M. Levsky
Esperanza Villanueva-Siles
Beverly A. Thornhill
Publication date: 01-09-2007
Publisher: Springer-Verlag
Published in: Pediatric Radiology / Issue 9/2007
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI: https://doi.org/10.1007/s00247-007-0535-9

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Springer Medicine

Spontaneous hemorrhage simulating rapid growth of a benign subperiosteal plexiform neurofibroma

Abstract

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Springer Medicine

Abstract

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