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Published in: Pediatric Radiology 10/2003

01-10-2003 | Case Report

Scimitar syndrome: complete anatomical and functional diagnosis with gadolinium-enhanced and velocity-encoded cine MRI

Authors: Enrique Marco de Lucas, Ana Canga, Pablo Sadaba, Rafael Martin-Duran, Macarena Otero, Luis Cerezal

Published in: Pediatric Radiology | Issue 10/2003

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Abstract

We report an asymptomatic 8-year-old girl with anomalous pulmonary venous connection to the IVC and systemic arterial supply (scimitar syndrome). We present for the first time a description of gadolinium-enhanced 3D MR angiography that provided concurrent non-invasive complete anatomical (arterial and venous supply) and 'functional' (calculation of left-to-right shunt using phase-contrast-MRI performed in the ascending aorta, main pulmonary artery and anomalous pulmonary vein) diagnosis, avoiding the need for more traditional invasive techniques. As the shunt quantification was less than 2:1, conservative management was decided upon.
Literature
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Metadata
Title
Scimitar syndrome: complete anatomical and functional diagnosis with gadolinium-enhanced and velocity-encoded cine MRI
Authors
Enrique Marco de Lucas
Ana Canga
Pablo Sadaba
Rafael Martin-Duran
Macarena Otero
Luis Cerezal
Publication date
01-10-2003
Publisher
Springer-Verlag
Published in
Pediatric Radiology / Issue 10/2003
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI
https://doi.org/10.1007/s00247-003-0951-4

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