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01-10-2003 | Diagnostic Neuroradiology

Cerebrofacial venous metameric syndrome (CVMS) 3: Sturge-Weber syndrome with bilateral lymphatic/venous malformations of the mandible

Authors: N. Ramli, M. Sachet, C. Bao, P. Lasjaunias

Published in: Neuroradiology | Issue 10/2003

Abstract

We present a case of Sturge-Weber syndrome with a bilateral lymphatic/venous malformation of the mandible. Modern biology suggests an explanation for such a case. The classification of cerebrofacial venous metameric syndromes (CVMS) enables us to recognise this lesion as involving the most caudal of the cranial metamere (CVMS 3).

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Title: Cerebrofacial venous metameric syndrome (CVMS) 3: Sturge-Weber syndrome with bilateral lymphatic/venous malformations of the mandible
Authors: N. Ramli
M. Sachet
C. Bao
P. Lasjaunias
Publication date: 01-10-2003
Publisher: Springer-Verlag
Published in: Neuroradiology / Issue 10/2003
Print ISSN: 0028-3940
Electronic ISSN: 1432-1920
DOI: https://doi.org/10.1007/s00234-003-1042-9

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Cerebrofacial venous metameric syndrome (CVMS) 3: Sturge-Weber syndrome with bilateral lymphatic/venous malformations of the mandible

Abstract

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Abstract

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