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Published in: International Urogynecology Journal 11/2017

01-11-2017 | IUJ Video

Vaginal vault prolapse in a patient with Mayer–Rokitansky–Küster–Hauser syndrome: a video case presentation

Authors: Carolyn Botros, Shilpa Iyer, Alexis M. Tran, Roger P. Goldberg

Published in: International Urogynecology Journal | Issue 11/2017

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Abstract

Introduction and hypothesis

Several reports have described vaginal prolapse in Mayer–Rokitansky–Küster–Hauser (MRKH) syndrome patients after creation of a neovagina. To our knowledge, no reports of primary vaginal prolapse of a blind pouch without previous intervention, or surgery for this condition, have been described.

Methods

In this case report, we describe a 19-year-old woman with MRKH and complete prolapse of her shortened vaginal pouch. Surgical correction utilizing permanent suture-based sacrospinous ligament fixation was performed.

Results

The patient had a successful outcome.

Conclusions

Sacrospinous ligament fixation provided a safe and effective method for the management of vaginal pouch prolapse. Long-term follow-up is planned. To our knowledge, this is the first report describing surgical repair of primary prolapse of a blind vaginal pouch in the setting of MRKH.
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Metadata
Title
Vaginal vault prolapse in a patient with Mayer–Rokitansky–Küster–Hauser syndrome: a video case presentation
Authors
Carolyn Botros
Shilpa Iyer
Alexis M. Tran
Roger P. Goldberg
Publication date
01-11-2017
Publisher
Springer London
Published in
International Urogynecology Journal / Issue 11/2017
Print ISSN: 0937-3462
Electronic ISSN: 1433-3023
DOI
https://doi.org/10.1007/s00192-017-3325-4

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