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Published in: Strahlentherapie und Onkologie 8/2017

01-08-2017 | Case Study

Successful treatment of a rare case of ameloblastic fibrosarcoma with radiation therapy

Authors: Michael Oertel, MD, Gabriele Reinartz, MD, Sergiu Scobioala, MD, Prof. Hans Theodor Eich, MD

Published in: Strahlentherapie und Onkologie | Issue 8/2017

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Abstract

Sarcomas are rare diseases of the head and neck region, representing around 1% of all malignancies. Amongst them, ameloblastic fibrosarcoma (AFS) is of even greater rarity, with less than 100 cases reported in the literature. Consequently, no standard treatment or guidelines have been made available. Surgery is often performed as primary therapy, but may be limited due to anatomical or functional reasons. We present a case of AFS successfully treated by postoperative radiation therapy. A detailed case study is provided, followed by a review of the English-language literature focusing on the role of radiation therapy.
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Metadata
Title
Successful treatment of a rare case of ameloblastic fibrosarcoma with radiation therapy
Authors
Michael Oertel, MD
Gabriele Reinartz, MD
Sergiu Scobioala, MD
Prof. Hans Theodor Eich, MD
Publication date
01-08-2017
Publisher
Springer Berlin Heidelberg
Published in
Strahlentherapie und Onkologie / Issue 8/2017
Print ISSN: 0179-7158
Electronic ISSN: 1439-099X
DOI
https://doi.org/10.1007/s00066-017-1136-7

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