Published in:
01-12-2017 | Correspondence
Rare Appearance, Rare Location and Unusual Patient Age
Report of Osteolytic Fibrous Dysplasia in the Temporal Bone of a 52-year-old Patient
Authors:
Viktor Pineker, Ewerton Marques Maggio, Alexander Huber, Athina Pangalu, Antonios Valavanis, Sebastian Winklhofer
Published in:
Clinical Neuroradiology
|
Issue 4/2017
Login to get access
Excerpt
Fibrous dysplasia (FD) is a benign developmental disorder in which normal bone is replaced by connective tissue and woven bone [
1]. In the head and neck region it may cause bone dysplasia, obstruction of sinuses and the skull foramina, as well as bony instability resulting in neural lesions, meningitis and malignant transformation. It is the most common genesis of bone dysplasia in childhood and young patients [
2]. There are three subtypes: the monostotic form (70%), affecting a single bone, the polyostotic form (25%), also known as Jaffé-Lichtenstein syndrome, affecting multiple bones and if the polyostotic form is combined with dermal hyperpigmentation and endocrine dysfunction it is classified as the rare McCune-Albright syndrome [
1]. …