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Published in: Journal of Maxillofacial and Oral Surgery 4/2023

24-11-2023 | Encephalocele | REVIEW PAPER

Ocular Hypertelorism: Principles and Management

Authors: Srinivas Gosla Reddy, Adity Bansal, Hermann F. Sailer, Likith V. Reddy, Ghali E. Ghali, Varsha Haridas Upadya

Published in: Journal of Maxillofacial and Oral Surgery | Issue 4/2023

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Abstract

Background

Ocular hypertelorism (OH) was initially considered as un-differentiated congenital cranio-facial deformity, however, I.T Jackson mentioned it as teleorbitism, considering it as increase in the inter-canthal width, inter-pupillary as well as inter-orbital distance as a result of lateralization of the orbital complex in total. Furthermore, Sailer further refined it and included the distance from the lateral orbital wall, i.e. he denoted increased inter-orbital distance along with the distance between lateral orbital walls as true hypertelorism. This condition is rare and is seen in association with midline congenital defects affecting the cranio-facial region.

Classification and review of cases

The ideal time for the OH correction is usually between 5 and 8 years of age. However, the management of OH is complex, and several techniques have been described in literature for the same. Here, we describe our classification of OH, along with the evolution of the surgical aspects, the key treatment principles we follow, together with the types of the osteotomies and their indications. Furthermore, we delineate the four main principles that we have set for OH management.

Results

Though the improvement in appearance is seen immediately post-surgery, however, this challenging surgery faces a multitude and common postoperative complications which have been represented in this article. The surgeon needs both the technical expertise and an inclination towards aesthetics for the execution of such procedures.

Conclusion

It is preferred that the management of OH should be individualized as per the stage of the craniofacial growth and the psychosocial needs of the patient and the parents.
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Metadata
Title
Ocular Hypertelorism: Principles and Management
Authors
Srinivas Gosla Reddy
Adity Bansal
Hermann F. Sailer
Likith V. Reddy
Ghali E. Ghali
Varsha Haridas Upadya
Publication date
24-11-2023
Publisher
Springer India
Keyword
Encephalocele
Published in
Journal of Maxillofacial and Oral Surgery / Issue 4/2023
Print ISSN: 0972-8279
Electronic ISSN: 0974-942X
DOI
https://doi.org/10.1007/s12663-023-02057-5

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