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Indian Journal of Hematology and Blood Transfusion

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01-06-2010 | Case Report

Factor VII Deficiency: A Rare Case Report

Authors: Ramanath Mahale, Pankaj Rathi, Chetan Ginegiri, Rajiv Aggarwal

Published in: Indian Journal of Hematology and Blood Transfusion | Issue 2/2010

Abstract

Factor VII deficiency is a rare congenital coagulopathy. Prolonged prothrombin time with normal partial thromboplastin time indicates factor VII deficiency. For the definitive diagnosis, the specific factor VII level should be investigated. We report a 20 day old, baby girl, born full-term who was admitted with the diagnosis of sepsis. Hematological tests revealed prolonged prothrombin time and a factor VII level of nine percent. After antibiotic therapy and fresh frozen plasma replacement, her clinical status improved but the prothrombin time continued to be prolonged. On the seventh day of discharge the baby died due to sudden intracranial hemorrhage.

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Title: Factor VII Deficiency: A Rare Case Report
Authors: Ramanath Mahale
Pankaj Rathi
Chetan Ginegiri
Rajiv Aggarwal
Publication date: 01-06-2010
Publisher: Springer-Verlag
Published in: Indian Journal of Hematology and Blood Transfusion / Issue 2/2010
Print ISSN: 0971-4502
Electronic ISSN: 0974-0449
DOI: https://doi.org/10.1007/s12288-010-0023-5

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