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Published in: Journal of Children's Orthopaedics 1/2010

01-02-2010 | Original Clinical Article

Gait in children with arthrogryposis multiplex congenita

Authors: Marie Eriksson, Elena M. Gutierrez-Farewik, Eva Broström, Åsa Bartonek

Published in: Journal of Children's Orthopaedics | Issue 1/2010

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Abstract

Purpose

Lower limb contractures and muscle weakness are common in children with arthrogryposis multiplex congenita (AMC). To enhance or facilitate ambulation, orthoses may be used. The aim of this study was to describe gait pattern among individuals wearing their habitual orthotic devices.

Methods

Fifteen children with AMC, mean age 12.4 (4.3) years, with some lower limb involvement underwent 3-D gait analysis. Three groups were defined based on orthosis use; Group 1 used knee–ankle–foot orthoses with locked knee joints, Group 2 used ankle–foot orthoses or knee–ankle–foot orthoses with open knee joints and Group 3 used no orthoses.

Results

The greatest trunk and pelvis movements in all planes and the greatest hip abduction were observed in Group 1, compared to Groups 2 and 3, as well as to the gait laboratory control group. Maximum hip extension was similar in Groups 1 and 2, but in Group 3, there was less hip extension and large deviations from the control data. Lower cadence and walking speed were observed in Group 1 than in Groups 2 and 3. The step length was similar in all groups and also with respect to the gait laboratory reference values.

Conclusions

Children with AMC were subdivided according to orthoses use. Kinematic data as recorded with 3-D gait analysis showed differences among the groups in trunk, pelvis and knee kinematics, and in cadence and walking speed. The step length was similar in all groups and to the gait laboratory reference values, which may be attributable to good hip extension strength in all participants.
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Metadata
Title
Gait in children with arthrogryposis multiplex congenita
Authors
Marie Eriksson
Elena M. Gutierrez-Farewik
Eva Broström
Åsa Bartonek
Publication date
01-02-2010
Publisher
Springer Berlin Heidelberg
Published in
Journal of Children's Orthopaedics / Issue 1/2010
Print ISSN: 1863-2521
Electronic ISSN: 1863-2548
DOI
https://doi.org/10.1007/s11832-009-0234-1

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