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Published in: Journal of Neuro-Oncology 3/2010

01-05-2010 | Case Report

A surgically treated case of Lhermitte–Duclos disease with a precise natural history and high uptake of FDG on PET

Authors: Yuko Goto, Naoya Hashimoto, Yoshiko Okita, Tetsu Goto, Carter Rabo, Hiroshi Hirayama, Yoshiharu Horikawa, Manabu Kinoshita, Naoki Kagawa, Toshiki Yoshimine

Published in: Journal of Neuro-Oncology | Issue 3/2010

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Abstract

We describe herein a surgically treated case of Lhermitte–Duclos disease in a 33-year-old man. The clinical presentation seemed typical in terms of symptoms, neurological signs, and neuroimaging. High and heterogenous fluorodeoxyglucose uptake in positron emission tomography study is presented and discussed. Furthermore, we performed volumetric analysis of the tumor with sequential magnetic resonance imaging over the course of 7 years before surgery, making this report the first with a long-term natural history, revealing that this rare disease entity may have a neoplastic nature.
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Metadata
Title
A surgically treated case of Lhermitte–Duclos disease with a precise natural history and high uptake of FDG on PET
Authors
Yuko Goto
Naoya Hashimoto
Yoshiko Okita
Tetsu Goto
Carter Rabo
Hiroshi Hirayama
Yoshiharu Horikawa
Manabu Kinoshita
Naoki Kagawa
Toshiki Yoshimine
Publication date
01-05-2010
Publisher
Springer US
Published in
Journal of Neuro-Oncology / Issue 3/2010
Print ISSN: 0167-594X
Electronic ISSN: 1573-7373
DOI
https://doi.org/10.1007/s11060-009-0042-y

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