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Neurological Sciences

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01-09-2021 | Vasculitis | Quiz Cases

Intramedullary lesion resection as an effective treatment of spinal cord microscopic polyangiitis: a case report

Authors: Zhiqian Yang, Dongpeng Cai, Yesheng Sun, Dequan Zhong, Hui Zhou, Deyuan Zhang, Wei Zhang

Published in: Neurological Sciences | Issue 9/2021

Abstract

Background

Microscopic polyangiitis (MPA), an autoimmune disease, is a subtype of anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis. The lungs and kidneys are the most common targets, whereas spinal cord involvement is rare.

Methods

We reported the clinical manifestations, diagnosis, and management of a patient with spinal cord MPA.

Results

The patient showed spinal compression symptoms and was diagnosed with MPA following magnetic resonance imaging (MRI) and histological examination. Spinal compression symptoms were completely relieved after intramedullary lesion resection and postoperative treatment with methylprednisolone.

Conclusion

The diagnosis of MPA without typical manifestations can be challenging. MRI and histological examination are of great importance in spinal cord MPA diagnosis. Intramedullary lesion resection is an effective treatment for spinal cord MPA. Methylprednisolone is also recommended for postoperative treatment.

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Title: Intramedullary lesion resection as an effective treatment of spinal cord microscopic polyangiitis: a case report
Authors: Zhiqian Yang
Dongpeng Cai
Yesheng Sun
Dequan Zhong
Hui Zhou
Deyuan Zhang
Wei Zhang
Publication date: 01-09-2021
Publisher: Springer International Publishing
Keywords: Vasculitis
Vasculitis
Magnetic Resonance Imaging
Neck and Back Pain
Magnetic Resonance Imaging
Published in: Neurological Sciences / Issue 9/2021
Print ISSN: 1590-1874
Electronic ISSN: 1590-3478
DOI: https://doi.org/10.1007/s10072-021-05103-7

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Intramedullary lesion resection as an effective treatment of spinal cord microscopic polyangiitis: a case report

Abstract

Background

Methods

Results

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Methods

Results

Conclusion

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