Top

European Journal of Orthopaedic Surgery & Traumatology

Published in:

01-05-2014 | Original Article

The natural history of focal fibrocartilaginous dysplasia in the young child with tibia vara

Authors: Vito Pavone, Gianluca Testa, Maria Riccioli, Andrea Sessa, Francesco Roberto Evola, Sergio Avondo

Published in: European Journal of Orthopaedic Surgery & Traumatology | Issue 4/2014

Abstract

Background

Focal fibrocartilaginous dysplasia is an uncommon disorder that affects young children causing unilateral deformity of the tibia. The lesion is seen in other similar conditions but this anomaly shows peculiar clinical characteristic.

Methods

Eleven young patients have been seen between the years 2002–2010 and followed up clinically and radiographically from 3 to 9 years. Family history, previous episode of trauma, infections, and bone disease in the children were not recountered.

Results

All cases were treated conservatively and self-corrected by the last follow-up. One case (9.09 %) displayed a 4° of varus, and one case (9.09 %) displayed a 5° of varus and one (9.09 %) a slight leg length discrepancy.

Conclusion

According to our results and those reported in the literature, focal fibrocartilaginous dysplasia is a benign affection that does not need treatment with a Levine and Drennan angle of <30°.

Bell SN, Campbell PE, Cole WG, Menelaus MB (1985) Tibia vara caused by focal fibrocartilaginous dysplasia. Three case reports. J Bone Joint Surg Br 67(5):780–784PubMed

Langenskiold A (1989) Tibia vara. A critical review. Clin Orthop Relat Res 246:195–207PubMed

Beaty JH, Barrett IR (1989) Unilateral angular deformity of the distal end of the femur secondary to a focal fibrous tether. A report of four cases. J Bone Joint Surg Am 71(3):440–445PubMed

Albinana J, Cuervo M, Certuchea JA et al (1997) Five additional cases of local fibrocartilafiuns dysplasia. J Pediatr Orthop B 6:52PubMedCrossRef

Eren A, Cakar M, Erol B, Özkurt A, Guvert M (2006) Focal fibrocartilaginous dysplasia in the humerus. J Pediatr Orthop B 15(6):449–452PubMedCrossRef

Lincoln TL, Birch JG (1997) Focal fibrocartilaginous dysplasia in the upper limb. J Pediatr Orthop 17:528–532PubMedCrossRef

Choi IH, Kim CJ, Cho TJ et al (2000) Focal fibrocartilaginous dysplasia of long bones: report of eight additional cases and literature review. J Pediatr Orthop 20(4):421–427PubMedCrossRef

Khanna G, Sundaram M, El-Khoury GY, Merkel K (2001) Focal fibrocartilaginous dysplasia: curettage as an alternative to conservative management or more radical surgery. Skeletal Radiol 30(7):418–421PubMedCrossRef

Smith NC, Carter PR, Ezaki M (2004) Focal fibrocartilaginous dysplasia in upper limb: seven additional cases. J Pediatr Orthop 24:700–705PubMedCrossRef

10.

Santos M, Valente E, Almada A, Neves J (2002) Tibia valga due to focal fibrocartilaginous dysplasia: case report. J Pediatr Orthop B 11:167–171PubMedCrossRef

11.

Brashid CF, Davies SJM, Malone M (1988) Tibia vara due to focal fibrocartilaginous dysplasia, the natural history. J Bone Joint Surg 70B:106–108

12.

Herman TE, Siegel MJ, McAlister WH (1990) Focal fibrocartilaginous dysplasia associated with tibia vara. Radiology 177(3):767–768PubMed

13.

Cockshott WP, Martin R, Friedman L, Yuen M (1994) Focal fibrocartilaginous dysplasia and tibia vara: a case report. Skeletal Radiol 23(5):333–335PubMedCrossRef

14.

Jouve JL, Kohler R, Mubarak SJ, Scott CN, Dohin B, Bollini G (2007) Focal fibrocartilaginous dysplasia (“fibrous periosteal inclusion”): an additional series of eleven cases and literature review. J Pediatr Orthop 27(1):75–84PubMedCrossRef

15.

Ringe KI, Schirg E, Rosenthal H, Berendonk H, Galanski M (2009) Unilateral tibia vara in toddler caused by focal fibrocartilaginous dysplasia. Pediatr Radiol 3(9):14–17

16.

Zayer M (1992) Tibia vara in fibrocartilaginous dysplasia. Acta Orthop Scand 63:353–355PubMedCrossRef

17.

Meyer JS, Davidson RS, Hubbard AM, Conard KA (1995) MRI of focal fibrocartilaginous dysplasia. J Pediatr Orthop 115:304–306CrossRef

18.

Dusabe JP, Docquier PL, Mousny M, Rombouts JJ (2006) Focal fibrocartilaginous dysplasia of the tibia: long-term evolution. Acta Orthop Belg 72:77–82PubMed

19.

Kim CJ, Choi IH, Cho TJ, Chung CY, Chi JG (1999) The histological spectrum of subperiosteal fibrocartilaginous pseudotumor of long bone (focal fibrocartilaginous dysplasia). Pathol Int 49(11):1000–1006PubMedCrossRef

20.

Olney BW, Cole WG, Menelaus MB (1990) Three additional cases of focal fibrocartilaginous dysplasia causing tibia vara. J Pediatr Orthop 10(3):405–407PubMedCrossRef

21.

Tavakoli A (2004) Tibia vara due to focal fibrocartilaginous dysplasia. J Res Med Sci 3:145–147

Title: The natural history of focal fibrocartilaginous dysplasia in the young child with tibia vara
Authors: Vito Pavone
Gianluca Testa
Maria Riccioli
Andrea Sessa
Francesco Roberto Evola
Sergio Avondo
Publication date: 01-05-2014
Publisher: Springer Paris
Published in: European Journal of Orthopaedic Surgery & Traumatology / Issue 4/2014
Print ISSN: 1633-8065
Electronic ISSN: 1432-1068
DOI: https://doi.org/10.1007/s00590-013-1346-3

Keynote webinar | Spotlight on medication adherence

Springer Medicine

The natural history of focal fibrocartilaginous dysplasia in the young child with tibia vara

Abstract

Background

Methods

Results

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Background

Methods

Results

Conclusion

Please log in to get access to this content

Other articles of this Issue 4/2014

Surgical treatment of lateral Hoffa fracture with a locking plate through the lateral approach

Megaprosthetic reconstruction for periprosthetic or highly comminuted fractures of the hip and knee

Tranexamic acid for reducing blood transfusions in arthroplasty interventions: a cost-effective practice

Amputation versus functional reconstruction in the management of complex hind foot injuries caused by land-mine explosions: a long-term retrospective comparison

Biomechanical parameters of the BP-enriched bone cement

Percutaneous versus open repair of acute Achilles tendon ruptures