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01-11-2005 | Rapid Communication

IgA nephropathy in an Italian child with familial Mediterranean fever

Authors: Donato Rigante, Gilda Federico, Pietro Ferrara, Nicola Maggiano, Laura Avallone, Anna Lisa Pugliese, Achille Stabile

Published in: Pediatric Nephrology | Issue 11/2005

Abstract

Familial Mediterranean fever is an autosomal recessive disorder characterized by transient attacks of fever and polyserositis with substantial risk of developing amyloidotic nephropathy over time. We report an Italian child with familial Mediterranean fever presenting with hematuria during attacks in whom kidney biopsy documented the presence of mesangial IgA deposits and the absence of amyloidosis. Kidney biopsy should be performed in patients showing microscopic or gross hematuria during attacks of familial Mediterranean fever in order to gain additional epidemiological data about specific features of renal involvement and to allow adequate treatment.

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Title: IgA nephropathy in an Italian child with familial Mediterranean fever
Authors: Donato Rigante
Gilda Federico
Pietro Ferrara
Nicola Maggiano
Laura Avallone
Anna Lisa Pugliese
Achille Stabile
Publication date: 01-11-2005
Publisher: Springer-Verlag
Published in: Pediatric Nephrology / Issue 11/2005
Print ISSN: 0931-041X
Electronic ISSN: 1432-198X
DOI: https://doi.org/10.1007/s00467-005-2023-5

Keynote webinar | Spotlight on medication adherence

Springer Medicine

IgA nephropathy in an Italian child with familial Mediterranean fever

Abstract

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

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