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Published in: Surgical Endoscopy 11/2006

01-11-2006

A laparoscopic approach to partial splenectomy for children with hereditary spherocytosis

Authors: S. Dutta, V. E. Price, V. Blanchette, J. C. Langer

Published in: Surgical Endoscopy | Issue 11/2006

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Abstract

Background

Partial splenectomy is sometimes used for children with hereditary spherocytosis (HS) to reduce hemolysis while retaining some splenic immune function. Previous reports have described a partial splenic resection through a laparotomy incision. Whereas laparoscopic total splenectomy for HS is well-established, laparoscopic partial splenectomy (LPS) has not been described. The authors have developed a novel LPS technique that combines the benefits of partial splenectomy with those of a laparoscopic approach.

Methods

A chart review was conducted for three children with HS who underwent LPS, with approximately one-fourth of the spleen left on the basis of the short gastric arterial supply.

Results

The mean preoperative spleen size was 17.6 cm. The mean preoperative hemoglobin count was 100 g/l, and the postoperative hemoglobin count was 133 g/l. All three patients reported reduced malaise and increased energy levels. There was no recurrent anemia at the 1- to 2-year follow-up evaluation.

Conclusion

The LPS procedure is a safe and effective approach to HS that resolves anemia, potentially retains some splenic immunity, and confers the benefits of a minimal access technique.
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Metadata
Title
A laparoscopic approach to partial splenectomy for children with hereditary spherocytosis
Authors
S. Dutta
V. E. Price
V. Blanchette
J. C. Langer
Publication date
01-11-2006
Publisher
Springer-Verlag
Published in
Surgical Endoscopy / Issue 11/2006
Print ISSN: 0930-2794
Electronic ISSN: 1432-2218
DOI
https://doi.org/10.1007/s00464-006-0131-3

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