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Published in: European Journal of Pediatrics 1/2022

01-01-2022 | Mitral Valve Replacement | Review

Paediatric mitral valve disease - from presentation to management

Authors: Sashini Iddawela, Prince Josiah Sajanthan Joseph, Roshan Ganeshan, Hussain Imtiaz Shah, Temitope Adebowale Temidayo Olatigbe, Anawinla Ta Anyu, Khaled Hadi, Abdulla Tarmahomed, Amer Harky

Published in: European Journal of Pediatrics | Issue 1/2022

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Abstract

Mitral valve diseases are relatively rare in the paediatric population; however, they can cause considerable mortality and morbidity worldwide. Acquired causes are a major contributor to cardiovascular disease burden in the paediatric population. Diseases can be detected before birth, at birth, or when the child is older and presents with symptoms of advanced heart failure. Definitive management consists of surgical intervention, with mitral valve replacement being the gold standard.
Conclusion: Repair has been gaining popularity; however, its outcomes require further study. Percutaneous mitral balloon valvuloplasty is an emerging technique which holds promise as a bridge to surgical treatment. The effect of these interventions on quality of life must be emphasised and requires further study.
What is Known:
• The epidemiology of mitral valve disease in the paediatric population - predominant causes include rheumatic disease and congenital defects. 
• Mitral valve repair and replacement are the standard treatment methods for paediatric mitral valve disease. 
What is New:
• Emergence of percutaneous mitral valve interventions and their potential as bridge-to-surgery or definitive treatment in high-risk surgical candidates. 
• Recent evidence comparing mitral valve repair and replacement in the paediatric population demonstrates increasing popularity of repair techniques. 
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Metadata
Title
Paediatric mitral valve disease - from presentation to management
Authors
Sashini Iddawela
Prince Josiah Sajanthan Joseph
Roshan Ganeshan
Hussain Imtiaz Shah
Temitope Adebowale Temidayo Olatigbe
Anawinla Ta Anyu
Khaled Hadi
Abdulla Tarmahomed
Amer Harky
Publication date
01-01-2022
Publisher
Springer Berlin Heidelberg
Published in
European Journal of Pediatrics / Issue 1/2022
Print ISSN: 0340-6199
Electronic ISSN: 1432-1076
DOI
https://doi.org/10.1007/s00431-021-04208-7

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