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01-11-2014 | Review

Hymenal anomalies in twins—review of the literature and case report

Authors: Rafal Watrowski, Christoph Jäger, Monika Gerber, Catherina Klein

Published in: European Journal of Pediatrics | Issue 11/2014

Abstract

Subocclusive hymenal variants, such as microperforate or septate hymen, impair somatic functions (e.g., vaginal intercourse or menstrual hygiene) and can negatively impact the quality of life of young women. We know little about the prevalence and inheritance of subocclusive hymenal variants. So far, eight cases of familial occurrence of occlusive hymenal anomalies (imperforate hymen) have been reported. In one of these cases, monozygotic twins were affected. We are reporting the first case of subocclusive hymenal variants (microperforate hymen and septate hymen) in 16-year-old white dizygotic twins. In addition, we review and discuss the current evidence. Conclusion: The mode of inheritance of hymenal variants has not been determined so far. Because surgical corrections of hymenal variants should be carried out in asymptomatic patients (before menarche), gynecologists and pediatricians should keep in mind that familial occurrences may occur.

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Title: Hymenal anomalies in twins—review of the literature and case report
Authors: Rafal Watrowski
Christoph Jäger
Monika Gerber
Catherina Klein
Publication date: 01-11-2014
Publisher: Springer Berlin Heidelberg
Published in: European Journal of Pediatrics / Issue 11/2014
Print ISSN: 0340-6199
Electronic ISSN: 1432-1076
DOI: https://doi.org/10.1007/s00431-013-2123-3

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Hymenal anomalies in twins—review of the literature and case report

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