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01-08-2021 | Glioma | Case Report

Cystic angiocentric glioma: a case report and literature review

Authors: Qiqi Wang, Yubo Xiong, Jun Chen, Qiang Shao

Published in: Child's Nervous System | Issue 8/2021

Abstract

Angiocentric glioma (AG) is a rare form of brain tumor characterized by cortical epileptogenic lesions that show angiocentric patterns upon histopathological examination. Cystoid degeneration is a rare radiological manifestation of this condition. We report a case involving the left eloquent cortical areas and review the clinical features of angiocentric glioma. A 10-year-old girl presented with a history of refractory drug-resistant epilepsy. Imaging revealed a cystic-solid neoplasm within the left frontal lobe. Surgical procedures were performed, and it was observed that the pathological manifestations were consistent with those of AG. Angiocentric glioma should be considered for diagnosis when the supratentorial cortical neoplasm contains a cystic component. The diagnosis of AG can be confirmed by histopathological examination. Gross total resection is the recommended strategy for controlling seizures elicited by this condition.

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Title: Cystic angiocentric glioma: a case report and literature review
Authors: Qiqi Wang
Yubo Xiong
Jun Chen
Qiang Shao
Publication date: 01-08-2021
Publisher: Springer Berlin Heidelberg
Keywords: Glioma
Glioma
Epilepsy
Glioma
Published in: Child's Nervous System / Issue 8/2021
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-020-04882-2

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Springer Medicine

Cystic angiocentric glioma: a case report and literature review

Abstract

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Abstract

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