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Child's Nervous System

Published in:

01-10-2011 | Special Annual Issue

Hydrocephalus and Chiari type I malformation

Authors: Concezio Di Rocco, Paolo Frassanito, Luca Massimi, Simone Peraio

Published in: Child's Nervous System | Issue 10/2011

Abstract

Intoduction

Hydrocephalus has been related to Chiari type I malformation (CIM) for a long time. The pathogenesis of this association is complex and still debated.

Discussion

A supratentorial hypertensive hydrocephalus may cause CIM, exerting pressure from above. Another pathogenetic hypothesis is based on the clinical and radiological data from patients affected by complex craniosynostosis, in which this association is more commonly observed as the consequence of a “cephalo-cranial disproportion” ultimately leading to a secondary hydrocephalus. In some cases, the concomitant presence of a stenosis of the jugular foramina would determine a condition of upward venous hypertension, resulting in the development of CIM and an associated hydrocephalus due to cerebellar parenchyma turgor.

Conclusions

The radiological association of ventricular enlargement and hindbrain herniation would be the result of heterogeneous pathogenetic mechanisms which would then require specific therapeutic approaches. In this context, the endoscopic third ventricle-cisternostomy is gaining an increasing interest because of its more physiologic correction of the altered CSF dynamics and its minor interference on the developmental processes responsible for the association of hydrocephalus and CIM.

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Title: Hydrocephalus and Chiari type I malformation
Authors: Concezio Di Rocco
Paolo Frassanito
Luca Massimi
Simone Peraio
Publication date: 01-10-2011
Publisher: Springer-Verlag
Published in: Child's Nervous System / Issue 10/2011
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-011-1545-3

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Hydrocephalus and Chiari type I malformation

Abstract

Intoduction

Discussion

Conclusions

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Intoduction

Discussion

Conclusions

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