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Published in: Child's Nervous System 1/2009

01-01-2009 | Case Report

Unusual cause of acute neurologic deficit in childhood: primary central nervous system vasculitis presenting with basilar arterial occlusion

Authors: Eren Kale Çekinmez, Nurcan Cengiz, İlknur Erol, Osman Kızılkılıç, Yasemin Uslu

Published in: Child's Nervous System | Issue 1/2009

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Abstract

Introduction

Primary central nervous system (CNS) vasculitis of childhood is a rare disorder. The most common signs and symptoms are acute severe headache and focal neurologic deficit. It should be suspected in children who have an acquired neurologic deficit that remains unexplained after an initial basic evaluation. Diagnosis usually depends on brain magnetic resonance imaging and conventional angiography of cerebral vasculature. Stenosis is the most common angiographic finding and it usually affects the middle cerebral artery and its branches. Anterior and posterior circulation is rarely involved.

Case report

In this report, we describe an 8-year-old boy who presented with vertebrobasilar insufficiency symptoms and primary CNS vasculitis diagnosis was made later.
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Metadata
Title
Unusual cause of acute neurologic deficit in childhood: primary central nervous system vasculitis presenting with basilar arterial occlusion
Authors
Eren Kale Çekinmez
Nurcan Cengiz
İlknur Erol
Osman Kızılkılıç
Yasemin Uslu
Publication date
01-01-2009
Publisher
Springer-Verlag
Published in
Child's Nervous System / Issue 1/2009
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI
https://doi.org/10.1007/s00381-008-0688-3

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