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Published in:

01-09-2006 | Case Report

Intracranial Rosai–Dorfman disease in a child mimicking bilateral giant petroclival meningiomas: a case report and review of literature

Authors: Deepak Kumar Gupta, Ashish Suri, Ashok Kumar Mahapatra, Veer Singh Mehta, Ajay Garg, Chitra Sarkar, Faiz U. Ahmad

Published in: Child's Nervous System | Issue 9/2006

Abstract

Objectives and importance

Rosai–Dorfman disease (RDD) is a rare but distinctive entity of unknown etiology; isolated intracranial RDD is uncommon. Of 37 reported intracranial RDD cases, only three were reported in children.

Clinical presentation

We report an unusual case of a 15-year-old boy presenting with 4 months history of raised intracranial pressure with visual deterioration. Computed tomography and magnetic resonance imaging revealed bilateral petroclival enhancing lesions with cavernous sinus extension mimicking meningioma. However, histological examination was diagnostic of RDD.

Intervention

The patient underwent extended right-sided middle fossa approach and near-total tumor removal from petroclival region and cavernous sinus on both sides in two stages 6 weeks apart.

Conclusion

Ours is the first case of pediatric isolated intracranial RDD presenting with giant bilateral petroclival masses successfully managed with bilateral extended middle fossa approach in two stages. An optimal treatment for RDD is not established, but complete surgical resection alone seems effective.

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Title: Intracranial Rosai–Dorfman disease in a child mimicking bilateral giant petroclival meningiomas: a case report and review of literature
Authors: Deepak Kumar Gupta
Ashish Suri
Ashok Kumar Mahapatra
Veer Singh Mehta
Ajay Garg
Chitra Sarkar
Faiz U. Ahmad
Publication date: 01-09-2006
Publisher: Springer-Verlag
Published in: Child's Nervous System / Issue 9/2006
Print ISSN: 0256-7040
Electronic ISSN: 1433-0350
DOI: https://doi.org/10.1007/s00381-006-0055-1

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Intracranial Rosai–Dorfman disease in a child mimicking bilateral giant petroclival meningiomas: a case report and review of literature

Abstract

Objectives and importance

Clinical presentation

Intervention

Conclusion

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

Objectives and importance

Clinical presentation

Intervention

Conclusion

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