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Published in: Surgical and Radiologic Anatomy 4/2009

01-04-2009 | Anatomic Variations

Scimitar syndrome with the left persistent superior vena cava

Authors: Jihong Sun, Shizheng Zhang, Dingyao Jiang, Guangzhao Yang

Published in: Surgical and Radiologic Anatomy | Issue 4/2009

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Abstract

Scimitar syndrome is a rare, complex congenital anomaly characterized by an anomalous connection of the pulmonary vein with the inferior vena cava (IVC). A persistent left superior vena cava (PLSVC) is another thoracic venous anomaly. We present a rare case with scimitar syndrome associated with the PLSVC. These variations were confirmed by magnetic resonance imaging (MRI) and computed tomography (CT). The typical features and the embryonic development of these variations are described. Radiological evaluations and clinical implications are discussed.
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Metadata
Title
Scimitar syndrome with the left persistent superior vena cava
Authors
Jihong Sun
Shizheng Zhang
Dingyao Jiang
Guangzhao Yang
Publication date
01-04-2009
Publisher
Springer-Verlag
Published in
Surgical and Radiologic Anatomy / Issue 4/2009
Print ISSN: 0930-1038
Electronic ISSN: 1279-8517
DOI
https://doi.org/10.1007/s00276-008-0403-9

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