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Abdominal Radiology
Published in: Abdominal Radiology 7/2015

01-10-2015 | Pictorial Essay

Spectrum of abdominal imaging findings in histiocytic disorders

Authors: Natally de Souza Maciel Rocha Horvat, Clovis Rego Coelho, Larissa Cardoso Roza, Rodrigo Canellas de Souza, Yves Bohrer Costa, Ebe Christie de Oliveira, Manoel de Souza Rocha, Ronaldo Hueb Baroni

Published in: Abdominal Radiology | Issue 7/2015

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Abstract

Objectives

The present article provides an overview of the spectrum of abdominal findings of histiocytic disorders that may be observed in multimodality imaging illustrated by clinical cases from our Imaging Center.

Methods

We will review abdominal findings of Langerhans cell histiocytosis, Rosai–Dorfman disease, Erdheim–Chester disease, and hemophagocytic syndrome illustrated by clinical cases from our imaging department with histologic correlation.

Results

Abdominal involvement of histiocytic disorders is rare and may occur in the liver, biliary tract, kidney, retroperitoneum, kidney, gastrointestinal tract, and lymph nodes.

Conclusion

Histiocytic disorders encompass a group of rare diseases with a wide range of manifestations in which the abdominal involvement is quite infrequent. The role of the radiologist is to report the major imaging findings and the differential diagnosis; however, the imaging features are unspecific and biopsy usually is necessary to establish the definitive diagnosis.
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Metadata
Title
Spectrum of abdominal imaging findings in histiocytic disorders
Authors
Natally de Souza Maciel Rocha Horvat
Clovis Rego Coelho
Larissa Cardoso Roza
Rodrigo Canellas de Souza
Yves Bohrer Costa
Ebe Christie de Oliveira
Manoel de Souza Rocha
Ronaldo Hueb Baroni
Publication date
01-10-2015
Publisher
Springer US
Published in
Abdominal Radiology / Issue 7/2015
Print ISSN: 2366-004X
Electronic ISSN: 2366-0058
DOI
https://doi.org/10.1007/s00261-015-0449-1

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