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Skeletal Radiology
Published in: Skeletal Radiology 11/2009

01-11-2009 | Review Article

Camurati–Engelmann disease: imaging, clinical features and differential diagnosis

Authors: Aldona Bartuseviciene, Arturas Samuilis, Jovitas Skucas

Published in: Skeletal Radiology | Issue 11/2009

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Abstract

We report four sporadic and three familial patients with Camurati–Engelmann disease. One patient had follow-up examinations over 8 years. Pain in the extremities and muscle weakness were common clinical symptoms. Most patients also had cranial nerve impairment, hepatosplenomegaly, a waddling gait, and elevated serum alkaline phosphatase levels. Long bones were affected in all. We discuss the differential diagnosis for this interesting bone entity.
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Metadata
Title
Camurati–Engelmann disease: imaging, clinical features and differential diagnosis
Authors
Aldona Bartuseviciene
Arturas Samuilis
Jovitas Skucas
Publication date
01-11-2009
Publisher
Springer Berlin Heidelberg
Published in
Skeletal Radiology / Issue 11/2009
Print ISSN: 0364-2348
Electronic ISSN: 1432-2161
DOI
https://doi.org/10.1007/s00256-008-0642-1

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