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Skeletal Radiology
Published in: Skeletal Radiology 9/2004

01-09-2004 | Case Report

Congenital (infantile) pseudarthrosis of the fibula associated with osteofibrous dysplasia

Authors: Masanori Hisaoka, Hiroshi Hashimoto, Takayuki Ohguri, Takatoshi Aoki, Sumika Okamoto, Hidetoshi Tanaka, Nobukazu Okimoto, Toshitaka Nakamura, Tsuyoshi Ishida

Published in: Skeletal Radiology | Issue 9/2004

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Abstract

We describe a recently noted association of congenital (infantile) pseudarthrosis of the lower leg with osteofibrous dysplasia. The patient was a 2-year-old boy who presented with a deformed left ankle joint and three cutaneous café-au-lait spots. Radiography demonstrated pseudarthrosis of the left distal fibula and a round lucent lesion adjacent to the proximal part of the pseudarthrosis. Histologically, the surgically removed fibula with pseudarthrosis showed a fibromatosis-like fibrovascular proliferation and nonspecific reparative changes. The focal lucent area demonstrated a fibro-osseous lesion, which was histologically identical to osteofibrous dysplasia. This case provides further evidence that osteofibrous dysplasia may be associated with congenital (infantile) pseudarthrosis of the lower leg.
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Metadata
Title
Congenital (infantile) pseudarthrosis of the fibula associated with osteofibrous dysplasia
Authors
Masanori Hisaoka
Hiroshi Hashimoto
Takayuki Ohguri
Takatoshi Aoki
Sumika Okamoto
Hidetoshi Tanaka
Nobukazu Okimoto
Toshitaka Nakamura
Tsuyoshi Ishida
Publication date
01-09-2004
Publisher
Springer-Verlag
Published in
Skeletal Radiology / Issue 9/2004
Print ISSN: 0364-2348
Electronic ISSN: 1432-2161
DOI
https://doi.org/10.1007/s00256-004-0759-9

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