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01-07-2010 | Case Report

Epithelioid hemangioendothelioma of the liver with metastatic coeliac lymph nodes in an 11-year-old boy

Authors: David Da Ines, Virginie Petitcolin, Juliette Joubert-Zakeyh, Francois Demeocq, Jean-Marc Garcier

Published in: Pediatric Radiology | Issue 7/2010

Abstract

Epithelioid hemangioendothelioma of the liver is a very rare vascular tumour in children with intermediate malignant potential. We present a case in which the typical imaging appearances of coalescent peripheral hepatic masses with capsular retraction contributed to the diagnosis. A positron emission tomography-CT (PET-CT) procedure was performed in staging the disease with a strong suspicion of coeliac nodal involvement confirmed after laparotomy and histological analysis. Our case is unique because of the rarity of the disease, the young age of the child, and proven nodal metastases at initial diagnosis. The use of PET-CT allows better staging at initial diagnosis and thus better management with improved follow-up in these patients.

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Title: Epithelioid hemangioendothelioma of the liver with metastatic coeliac lymph nodes in an 11-year-old boy
Authors: David Da Ines
Virginie Petitcolin
Juliette Joubert-Zakeyh
Francois Demeocq
Jean-Marc Garcier
Publication date: 01-07-2010
Publisher: Springer-Verlag
Published in: Pediatric Radiology / Issue 7/2010
Print ISSN: 0301-0449
Electronic ISSN: 1432-1998
DOI: https://doi.org/10.1007/s00247-009-1532-y

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Epithelioid hemangioendothelioma of the liver with metastatic coeliac lymph nodes in an 11-year-old boy

Abstract

Keynote webinar | Spotlight on medication adherence

Springer Medicine

Abstract

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